Proximal femoral focal deficiency as a manifestation of Antley-Bixler syndrome: a case report.

نویسندگان

  • A R Sulaiman
  • H Nawaz
  • I Munajat
  • A Y Sallehudin
چکیده

We report a case of the Antley-Bixler syndrome in an 11-year-old girl. She presented with bilateral proximal femoral focal deficiency, right clubfoot, left radiohumeral synostosis, bilateral ear hypoplasia, cleft palate, tongue tie, missing teeth, congenital heart disease, a pelvic kidney with hydronephrosis, and mental retardation. Proximal femoral focal deficiency has never been reported before as a manifestation of Antley-Bixler syndrome. Her mother was exposed to radiation during an intravenous urogram done in the first trimester of pregnancy. Exposure to radiation has not been implicated as a cause of Antley-Bixler syndrome.

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Prenatal Diagnosis of Antley-Bixler Syndrome and POR Deficiency

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Original articles Evidence for digenic inheritance in some cases of Antley-Bixler syndrome?

The Antley-Bixler syndrome has been thought to be caused by an autosomal recessive gene. However, patients with this phenotype have been reported with a new dominant mutation at the FGFR2 locus as well as in the oVspring of mothers taking the antifungal agent fluconazole during early pregnancy. In addition to the craniosynostosis and joint ankylosis which are the clinical hallmarks of the condi...

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عنوان ژورنال:
  • Journal of orthopaedic surgery

دوره 15 1  شماره 

صفحات  -

تاریخ انتشار 2007